Acute Type A Aortic Dissection during Late Pregnancy Period in a Patient with Marfan's Syndrome

VernacularTitle:妊娠38週で急性 A 型大動脈解離を発症した Marfan 症候群の1例
Author: Hideaki YAMABI ¹ ; Akitoshi INUI ¹ ; Takahiro MATSUOKA ¹ ; Kousuke SIGEMATSU ² ; Kazuhito IMANAKA ¹
Author Information

1. Department of Cardiovascular Surgery, Saitama Medical Center, Saitama Medical University
2. Center for Maternal Fetal and Neonatal Medicine, Saitama Medical Center, Saitama Medical University
Keywords: Marfan syndrome; acute aortic dissection; Stanford type A; AAE; pregnancy
From:Japanese Journal of Cardiovascular Surgery 2019;48(6):425-427
CountryJapan
Language:Japanese
Abstract: A 34-year-old female with a gestational age of 38 weeks developed acute type A aortic dissection. Appearance of this patient was typical for Marfan's syndrome, and echocardiography revealed annulo-aortic ectasia with mild aortic regurgitation, but pericardial effusion was absent. As her hemodynamic condition was stable, an emergency Caesarean section was carried out first. After careful observation in the ICU for half a day, she successfully underwent aortic valve reimplantation and replacement of the ascending aorta under deep hypothermic circulatory arrest. Intraoperative heparin use minimally impacted uterine bleeding. Both the mother and the neonate were discharged home 16 days later. We believe a two-stage strategy should be adopted whenever possible.