Mesenteric fibromatosis: report of 7 cases
10.3760/cma.j.issn.1007-631X.2019.07.007
- VernacularTitle:肠系膜侵袭性纤维瘤病七例临床分析
- Author:
Feng LIU
1
;
Xiaoyang WU
;
Xiaojun SHEN
Author Information
1. 昆山市第一人民医院胃肠外科
- Keywords:
Fibromatosis,aggressive;
Mesentery;
Surgical procedures,operative
- From:
Chinese Journal of General Surgery
2019;34(7):580-582
- CountryChina
- Language:Chinese
-
Abstract:
Objective To invastigate the etiology,diagnosis and treatment of mesenteric fibromatosis.Methods 7 cases of mesenteric fibromatosis was admitted into our hospital from Jan 2012 to Jan 2018.Reslut Among the 7 patients,there were 2 males and 5 females,with an average age of (40 + 16)years,4 cases had had a history of abdominal surgery and 1 case was of familial polyp,the symptoms of organ compression were the first manifestation in 4 cases,abdominal mass as the first manifestation in 2 cases.The lesions were located on small mesentery in 5 cases,on mesenteric membrane in one,and on mesorectal membrane in one.All 7 patients underwent extensive tumor resection and the margins were negative,one of the tumors was located at the level of the duodenum,invading the superior mesenteric vein and the transverse mesocolon.Immunohistochemistry results:[3-catenin (+)、Ki-67 (+),CD117 (-),CD34(-)in7 cases,SMA(+)in5 cases,Desmin (+) in4 cases,ER (+) in3 cases.Conclusion Most patients of mesenteric fibroma have a history of previous abdominal surgery,seconded by organ compression symptoms.β-catenin (+),Ki-67 (+) and CD117 (-),CD34 (-) contribute to pathological diagnosis,Surgery-based comprehensive treatment can achieve therapeutic effect.
