Research progress of idiopathic systemic capillary leakage syndrome
10.3969/j.issn.1008-9691.2019.04.038
- VernacularTitle:特发性系统性毛细血管渗漏综合征研究进展
- Author:
Yueqin WU
1
;
Dongqiang WANG
;
Zhijun LI
Author Information
1. 天津市第一中心医院中西医结合科
- Keywords:
Idiopathic systemic capillary leakage syndrome;
Recurrence;
Research progress
- From:
Chinese Journal of Integrated Traditional and Western Medicine in Intensive and Critical Care
2019;26(4):510-512
- CountryChina
- Language:Chinese
-
Abstract:
Idiopathic systemic capillary leak syndrome (ISCLS) is a rare disease, the clinical manifestation is increased acute episodic capillary leakage (SCL), leading to protein-rich fluid leakage from the blood vessels to the interstitial tissue space, resulting in progressive systemic edema, hypoproteinemia, hypotension, blood concentration and other clinical symptoms. Because of ISCLS frequent recurrences, high mortality, pathogenesis unclear and no definite treatment plan, it is extremely important to fully understand the disease to carry out early intervention to save the patients' lives. This article reviews the progress of ISCLS, including its disease onset characteristics, clinical features, pathological mechanism, diagnosis and treatment of ISCLS.
