One case report on VHL disease with multiple cysts of the pancreas as the main symptom
10.3760/cma.j.issn.1674-6090.2019.03.019
- VernacularTitle:以胰腺多发囊肿为主要症状的VHL病一例报告并文献复习
- Author:
Youwei LI
1
;
Hui XIE
;
Gang MAI
;
Shan LIU
;
Chun MA
;
Fengfen LIU
;
Jie TAN
Author Information
1. 德阳市人民医院 618000
- Keywords:
VHL disease;
Hemangioblastoma;
Pancreatic cyst
- From:
Chinese Journal of Endocrine Surgery
2019;13(3):259-262
- CountryChina
- Language:Chinese
-
Abstract:
Von Hippel-Lindau (VHL) disease is a benign or malignant tumor syndrome which involves multiple systems and organs.Recently,a patient was diagnosed and hospitalized with an initial clinical symptom of pancreatic multiple cystic space-occupying.Multidisciplinary examination and consultation confirmed that there were hemangioblastomas in cerebella,spinal cord and retina,but with no clinical symptoms;therefore,it was diagnosed as VHL disease.According to previous case reports,only a few single cases revealed lesions in so many parts of the central nervous system with typical imaging manifestations.We present an overview and aim to improve the diagnosis of VHL disease with the initial clinical symptom of pancreatic lesions.
