Primary uterine angiosarcoma with “rhabdoid morphology”: A case report
- Author:
Jatin S Gandhi
1
,
2
,
3
Author Information
1. Department of Histopathology &
2. Cytopathology, Rajiv Gandhi Cancer Institute &
3. Research Center, Sector 5 Rohini, New Delhi-85, India.
- Collective Name:Jatin S Gandhi; Meenakshi Kamboj; Gurudutt Gupta and Neha Seth
- Publication Type:Case Reports
- Keywords:
Angiosarcoma;
uterus;
rhabdoid
- MeSH:
Angiosarcoma
- From:The Malaysian Journal of Pathology
2018;40(2):203-207
- CountryMalaysia
- Language:English
-
Abstract:
Introduction: Primary uterine angiosarcoma is a very rare tumour, with only 23 cases described till now. It is a malignant tumour with cells variably recapitulating the morphologic features of an endothelium and expressing immunohistochemical markers of endothelial cells. In general, it is a bulky neoplasm and frequently is at advance stage of disease at presentation. In general, patients with uterine angiosarcoma tend to have a poorer prognosis, mostly related to the aggressive nature and the metastatic potential of these tumours. Case report: We report a rare case of primary uterine angiosarcoma with unusual rhabdoid morphology in a 41-year-old female, who underwent radical hysterectomy and died of disease after 4 months of treatment. Discussion: We described the differential diagnosis of primary angiosarcoma of the uterus that can pose a diagnostic challenge.
- Full text:5.2018my0969.pdf