Surgical treatment strategy and outcome of functional univentricular heart with total anomalous pulmonary vein drainage
- VernacularTitle:功能性单心室合并完全性肺静脉异位引流的外科策略与结果
- Author:
DU Xinwei
1
,
2
;
SUN Yanjun
1
,
2
;
ZHU Zhongqun
1
,
2
;
ZHU Hongbin
1
,
2
;
ZHENG Jinghao
1
,
2
;
ZHANG Haibo
1
,
2
;
XU Zhiwei
1
,
2
;
WANG Shunming
1
,
2
Author Information
- Publication Type:Journal Article
- Keywords: Functional single ventricle; anomalous pulmonary vein drainage; pulmonary vein obstruction
- From: Chinese Journal of Clinical Thoracic and Cardiovascular Surgery 2018;25(2):118-122
- CountryChina
- Language:Chinese
- Abstract: Objective To explore the surgical management method and outcome of functional univentricular heart with total anomalous pulmonary vein drainage (UVH-TAPVD). Methods We reviewed the surgical procedures and results for 44 UVH-TAPVD patients in our hospital between the year 2010 and 2016. There were 34 males and 10 females. The age of the patients was 312 (77-4 220) d when they accepted the first surgical treatment. Results There were 8 deaths in stage Ⅰ palliation, 1 death in stage Ⅱ palliation and 5 deaths during the follow-up. The overall survival rate was 68.2% (30/44). Glenn operation was undertaken in 34 patients with 5 deaths. Fontan operation was undertaken in 9 patients with 2 deaths. Conclusion Surgical strategies for UVH-TAPVD should be planned according to different anatomical and pathophysiological conditions in different patients. Staged palliations can reduce mortality and morbidity. But pulmonary venous obstruction and heterotaxy syndrome are still risk factors for these patients.
