Radius-Maumenee Syndrome Presenting with Ocular Pain and Conjunctival Injection: A Case Report.
10.3341/jkos.2015.56.12.1969
- Author:
Byeong Soo KANG
1
;
Eun Ji LEE
;
Hee Kyung YANG
Author Information
1. Department of Ophthalmology, Seoul National University College of Medicine, Seoul, Korea. eye@snubh.org
- Publication Type:Case Report
- Keywords:
Dilated episcleral vein;
Open angle glaucoma;
Radius-Maumenee syndrome
- MeSH:
Adult;
Brain;
Diagnosis;
Eye Pain;
Fistula;
Glaucoma;
Glaucoma, Open-Angle;
Humans;
Hyperemia;
Magnetic Resonance Angiography;
Magnetic Resonance Imaging;
Male;
Nerve Fibers;
Orbit;
Retinaldehyde;
Scotoma;
Visual Acuity;
Visual Field Tests
- From:Journal of the Korean Ophthalmological Society
2015;56(12):1969-1973
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
PURPOSE: Radius-Maumenee syndrome (RMS) is characterized by idiopathic dilated episcleral vessels usually associated with glaucoma. The authors report a case of a 32-year-old Korean male with dilation of the episcleral vessels and glaucoma in both eyes. CASE SUMMARY: A 32-year-old Korean male presented with conjunctival injection and chronic pulsatile ocular pain in both eyes for 11 years. His best corrected visual acuity was 20/20 in both eyes. Slit lamp biomicroscopy showed episcleral venous engorgement in both eyes. Fundus photographs revealed superotemporal and inferotemporal retinal nerve fiber layer defects and Humphrey visual field testing showed superior nasal steps and paracentral scotomas in both eyes. He suffered from chronic eye pain in both eyes although he had applied glaucoma medication and his symptoms had worsened during the past year. Brain magnetic resonance imaging (MRI) and magnetic resonance angiography (MRA) revealed no evidence of carotid cavernous fistula or other orbital lesions. Due to the presence of episcleral venous engorgement, glaucoma and negative tests for other possible diseases, he was diagnosed with RMS. CONCLUSIONS: RMS is an idiopathic disease with episcleral vessel dilation and frequently associated with glaucoma. Its diagnosis is confirmed by eliminating other possible causes of episcleral venous engorgement.
