A case of relapsing polychondritis with vasculitis mimicking Takayasu's arteritis.
- Author:
Jeong Jin PARK
1
;
Jung Chan LEE
;
Hyo Jin CHOI
;
Churl Hyun IM
;
Eun Ha KANG
;
Eun Bong LEE
;
Yeong Wook SONG
Author Information
1. Department of Internal Medicine, College of Medicine, Seoul National University, Seoul, Korea. ysong@snu.ac.kr
- Publication Type:Case Report
- Keywords:
Relapsing polychondritis;
Aortitis;
Takayasu's arteritis
- MeSH:
Aorta;
Aortic Aneurysm;
Aortitis;
Autoimmune Diseases;
Ear;
Heart;
Humans;
Inflammation;
Joints;
Middle Aged;
Mitral Valve Insufficiency;
Nose;
Polychondritis, Relapsing*;
Respiratory System;
Skin;
Takayasu Arteritis*;
Vasculitis*
- From:Korean Journal of Medicine
2004;67(Suppl 3):S732-S735
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Relapsing polychondritis is a rare autoimmune disease of unknown etiology characterized by recurrent inflammation of cartilaginous structures of the ears, nose, respiratory tract and joints. Relapsing polychondritis may affect proteoglycan-rich tissues, such as the eyes, aorta, heart, and skin. Several cardiovascular complications have been reported in patients with relapsing polychondritis. The most common findings of cardiovascular manifestations are aortic or mitral regurgitation and aortic aneurysm. Aortitis is a very rare complication of relapsing polychondritis. We report a case of 48-year-old man who had relapsing polychondritis with aortitis mimicking Takayasu's arteritis.