Prognosis of the complete transposition of great arteries with left ventricular outflow tract obstruction after intraventricular repair
10.7507/1007-4848.201808048
- VernacularTitle:完全性大动脉转位合并左室流出道狭窄患儿行不同心室内修复手术的回顾性队列研究
- Author:
XING Yunchao
1
,
2
;
LI Shoujun
1
,
2
;
YAN Jun
1
,
2
;
WANG Xu
1
,
2
;
YAN Fuxia
1
,
2
;
YI Tong
1
,
2
;
JIANG Xianchao
1
,
2
;
MA Zhiling
1
,
2
;
WANG Qiang
1
,
2
Author Information
1. Pediatric Cardiac Surgical Centre, Cardiovascular Institute and Fuwai Hospital, Chinese Academy of Medical Sciences &
2. Peking Union Medical College, Beijing, 100037, P.R.China
- Publication Type:Journal Article
- Keywords:
Complete transposition of great arteries;
left ventricular outflow tract obstruction;
intraventricular repair;
prognostic analysis
- From:
Chinese Journal of Clinical Thoracic and Cardiovascular Surgery
2019;26(6):534-538
- CountryChina
- Language:Chinese
-
Abstract:
Objective To compare the clinical characteristics and prognosis of patients who received two different intraventricular repair. Methods We retrospectively analyzed the clinical data of 24 complete transposition of the great arteries (TGA)/left ventricular outflow tract obstruction (LVOTO) patients who all received intraventricular repair. The patients were allocated into two groups including a REV group and a Rastelli group. There were 13 patients with 9 males and 4 females at median age of 25.2 (6, 72) months in the REV group. There were 11 patients with 10 males and 1 female at median age of 47.9 (14, 144) months in the Rastelli group. Results The age at operation (P=0.041), pulmonary valve Z value (P=0.002), and LVOT gradient (P=0.004), rate of multiphase operation between the REV group and the Rastelli group was statistically different. The mean follow-up time was 17.3 months. And during the follow-up, 1 patient had early mortality, 2 patients had early reintervention, 7 patients had postoperative RVOTO, and received Rastelli and larger VSD inner diameter were associated with postoperative RVOTO. Conclusion As the traditional surgery for TGA/LVOTO patients, the intraventricular repair has a low early mortality and low early reintervention. Modified REV is associated with postoperative peripheral pulmonary vein isolation (PVIS). Patients who received Rastelli operation and with larger VSD inner diameter are more likely to have postoperative RVOTO, but the reintervention for PVI and RVOTO during follow up is very low.