A Case of Alveolar Soft Part Sarcoma in a Child.
- Author:
Jee Yong KIM
1
;
Geun Young LEE
;
Ok Ran SHIN
;
Ju Mee KANG
;
Pil Sang JANG
;
Dong Un KIM
;
Young Hoon KIM
;
Jin Tack KIM
Author Information
1. Department of Pediatrics, College of Medicine, The Catholic University of Korea, Seoul, Korea. drmagic@catholic.ac.kr
- Publication Type:Case Report
- Keywords:
Alveolar soft part sarcoma;
Children
- MeSH:
Child*;
Drug Therapy;
Humans;
Neoplasm Metastasis;
Radiotherapy;
Sarcoma;
Sarcoma, Alveolar Soft Part*;
Viperidae
- From:Korean Journal of Pediatric Hematology-Oncology
2004;11(2):260-264
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Alveolar soft part sarcoma (ASPS) is a rare soft tissue tumor that accounts for 5% of pediatric non-rhabdomyosarcoma soft tissue sarcomas. The disease presents as a indolent asymptomatic mass and affects primarily younger patients. The clinical course is often indolent and late metastases can develop even after prolonged disease-free intervals. Radiotherapy and chemotherapy play a very limited role in the treatment. We report a pediatric case of ASPS with a brief review of the literature.
