Moyamoya disease in a 3-year-old boy presenting with a focal motor seizure provoked by hyperventilation
- Author:
Soojin HWANG
1
;
Jung Heon KIM
;
Hee Mang YOON
;
Mi Sun YUM
Author Information
- Publication Type:Case Report
- Keywords: Angiography; Emergencies; Hyperventilation; Ischemia; Moyamoya Disease; Seizures; Stroke; Vasoconstriction
- MeSH: Angiography; Brain Ischemia; Carotid Artery, Internal; Child; Child, Preschool; Constriction, Pathologic; Crying; Diagnosis; Emergencies; Emergency Service, Hospital; Extremities; Frontal Lobe; Head; Hospitalization; Humans; Hyperventilation; Infarction; Ischemia; Magnetic Resonance Imaging; Male; Moyamoya Disease; Seizures; Stroke; Vasoconstriction
- From:Pediatric Emergency Medicine Journal 2018;5(1):25-29
- CountryRepublic of Korea
- Language:English
- Abstract: A previously healthy, 3-year-old boy presented to the emergency department with an afebrile focal motor seizure. He was found crying and having a seizure 30 minutes earlier. During this seizure, he was jerking his head and right extremities. Subsequent magnetic resonance imaging showed acute infarction in the bilateral frontal lobes, chiefly in the left. After hospitalization, conventional angiography demonstrated bilateral stenosis of the distal internal carotid arteries with development of lenticulostriate collaterals, which confirmed the diagnosis of moyamoya disease. It is vital to recognize focal motor seizures and situations related to hyperventilation in children with a seizure, which imply a structural lesion and a provoked cerebral ischemia in preexisting moyamoya disease, respectively.
