Idiopathic Granulomatous Hypophysitis with Rapid Onset: A Case Report

Author: Hyun Joo PARK ¹ ; Sung Hye PARK ; Jung Hee KIM ; Yong Hwy KIM
Author Information

1. Department of Neurosurgery, Seoul National University College of Medicine, Seoul, Korea. kimyh96@snu.ac.kr
Publication Type:Case Report
Keywords: Pituitary gland; Hypophysitis; Glucocorticoids; Sella turcica; Endoscopy; Adult
MeSH: Adult; Autoimmune Hypophysitis; Craniopharyngioma; Endoscopy; Glucocorticoids; Hand; Headache; Humans; Pituitary Gland; Pituitary Neoplasms; Rare Diseases; Sella Turcica; Tuberculoma
From:Brain Tumor Research and Treatment 2019;7(1):57-61
CountryRepublic of Korea
Language:English
Abstract: Idiopathic granulomatous hypophysitis (IGH), a rare disease, requires differentiation from more common mass lesions of the sella such as pituitary adenoma, craniopharyngioma, Rathke's cleft cyst, or pituitary tuberculoma. IGH usually presents with an insidious onset of visual defects and headaches. On the other hand, rapid onset of neurologic and visual symptoms in an IGH patient is exceptionally rare. Here, we present a biopsy-proven case of IGH with rapid onset and satisfactory outcome after high dose steroid treatment.