Research progress on neonatal lymphatic dysplasia
10.3760/cma.j.issn.1673-4408.2019.01.012
- VernacularTitle:新生儿淋巴管发育异常研究进展
- Author:
Siyao WANG
1
Author Information
1. 中国医科大学附属盛京医院第二新生儿内科
- Keywords:
Newborn;
Lymphatic dysplasia;
Chylothorax
- From:
International Journal of Pediatrics
2019;46(1):48-52
- CountryChina
- Language:Chinese
-
Abstract:
Neonatal lymphatic dysplasia is a congenital maldevelopment,causing effusion of chyle or lymph into the limbs or into the pleural,pericardial or peritoneal cavities,forming chylothorax ascites or edema,resulting in immunodeficiency and malnutrition.Neonatal lymphatic dysplasia is rare in neonate,but associated with significant mortality.So far,the etiology and pathological mechanism are still unclear.Lymphoscintigraphy is a diagnostic tool in newborns to obtain early diagnosis.Octreotide has been proposed for treatment of lymphatic dysplasia recently,however,the effiency and safety remain controversial.This article is to review the update in diagnosis and treatment of neonatal lymphatic disorders.