Progress in the diagnosis and treatment of Kartagener syndrome in children
10.3760/cma.j.issn.1673-4408.2018.12.009
- VernacularTitle:儿童Kartagener综合征的诊治新进展
- Author:
Lin LI
1
;
Chenguang QIN
Author Information
1. 中国人民解放军武汉中部战区总医院儿科
- Keywords:
Kartagener syndrome;
Primary ciliary dyskinesia;
Children;
Gene;
Cilia
- From:
International Journal of Pediatrics
2018;45(12):937-940
- CountryChina
- Language:Chinese
-
Abstract:
Kartagener syndrome is a rare autosomal recessive disease with low incidence.Clinically,typical visceral inversion,bronchiectasis and sinusitis triad are typical.The pathogenesis of the disease is not clear.The principle of treatment is mainly symptomatic treatment,postponing the progress of bronchiectasis,Lack of fundamental treatment.The disease generally has a good prognosis.This article reviews recent advances in the diagnosis and treatment of Kartagener syndrome at home and abroad.
