Progress in the diagnosis and treatment of hepatopulmonary syndrome in children
10.3760/cma.j.issn.1673-4408.2018.12.001
- VernacularTitle:儿童肝肺综合征的诊断及治疗研究进展
- Author:
Zhengli LI
1
Author Information
1. 100020,首都儿科研究所附属儿童医院呼吸内科
- Keywords:
Hepatopulmonary syndrome;
Children;
Diagnosis;
Treatment
- From:
International Journal of Pediatrics
2018;45(12):903-906
- CountryChina
- Language:Chinese
-
Abstract:
Hepatopulmonary syndrome (HPS) is a group of rare and serious complications caused by liver disease,which is summarized as "progressive chronic liver disease,pulmonary vasodilatation,abnormal gas exchange leading to arterial hypoxemia".Progressive hypoxemia causes high mortality in children with HPS,and liver transplantation is the only effective cure method.At present,there are few research on HPS in children,especially in China.The possible etiology,pathogenesis,clinical characteristics,diagnosis and detection methods,treatment and prognosis are reviewed in this paper.
