A Rare Presentation of Plexiform Neurofibroma
- Author:
Poh KW
1
;
Syed Osman SIH
Author Information
1. Department of Ophthalmology, Hospital Kuala Lumpur, Jalan Pahang, 50586 Kuala Lumpur, Malaysia.
- Publication Type:Case report
- Keywords:
Conjunctiva;
eyelids;
lacrimal gland;
neurofibromatosis;
plexiform neurofibroma
- From:Journal of Surgical Academia
2018;8(1):39-42
- CountryMalaysia
- Language:English
-
Abstract:
We report on a rare case of a child with persistent right upper lid eversion with conjunctival prolapse since birth that failed various attempts in repositioning the right superior fornix at other centre. He was found to have a right supero-temporal orbital mass above the prolapsed area. Computerized tomography (CT) scan of orbit confirmed a right lacrimal gland tumour with thinning of the right lesser wing of sphenoid. An excision biopsy of the tumour via anterior orbitotomy and eyelid reconstruction were performed. Histopathology report reviewed plexiform neurofibroma of the lacrimal gland. Further physical examination confirmed presence ofmultiple café-au-lait spots. He was diagnosed as Neurofibromatosis Type 1
