Phacomatosis Pigmentovascularis Type II: Case Report
- Author:
Kit Wan WONG
1
;
Kwee Eng TEY
Author Information
1. Department of Dermatology, Hospital Sultanah Aminah, Johor Bahru, Johor, Malaysia
- Publication Type:Case Report
- Keywords:
Phacomatosis pigmentovascularis;
Klippel-Trenaunay syndrome
- From:Malaysian Journal of Dermatology
2018;40(June):69-72
- CountryMalaysia
- Language:English
-
Abstract:
Phacomatosis pigmentovascularis is a rare syndrome first described by Ota et al, in 1947. It ischaracterized by a combination of capillary malformation and other pigmented naevi. It had originallybeen classified into four major types. A fifth type, in which the vascular lesion is cutis marmoratatelangiectatica congenita (CMTC), was subsequently added. Each type was further categorizedaccording to the absence or presence of associated extra-cutaneous signs as types (a) and (b),respectively. We reported this case due to its rare clinical presentation, with probable overlap Klippel-Trenaunay syndrome.
