Perivascular epithelioid cell tumor (PEComa) of the ascending colon: the implication of IFN-alpha2b treatment.
10.3345/kjp.2010.53.11.975
- Author:
Sun Ju PARK
1
;
Dong Kyun HAN
;
Hee Jo BAEK
;
Sang Young CHUNG
;
Jong Hee NAM
;
Hoon KOOK
;
Tai Ju HWANG
Author Information
1. Department of Pediatrics, Chonnam National University Hwasun Hospital, Chonnam National University Medical School, Gwangju, Korea. hoonkook@chonnam.ac.kr
- Publication Type:Case Report
- Keywords:
Perivascular epithelioid cell tumor;
PEComa;
Colon;
Interferon-alpha
- MeSH:
Abdominal Pain;
Child;
Colon;
Colon, Ascending;
Colonoscopy;
Epithelioid Cells;
Gastrointestinal Hemorrhage;
Humans;
Immunotherapy;
Interferon-alpha;
Perivascular Epithelioid Cell Neoplasms
- From:Korean Journal of Pediatrics
2010;53(11):975-978
- CountryRepublic of Korea
- Language:English
-
Abstract:
A 7-year-old boy presented with hematochezia and abdominal pain. A 3.7-cm-sized mass was identified in the ascending colon by abdominal computed tomography and colonoscopy. The patient underwent surgical resection. Pathological examination revealed a low-grade perivascular epithelioid cell tumor (PEComa). PEComa in the colon is very rare. Only a few cases have been reported so far. An effective treatment method for this rare tumor has not been established yet. The patient received adjuvant interferon-alpha immunotherapy for 1 year. He has been tumor-free for 26 months since the initial diagnosis. This report is the first documented case of the use of interferon-alpha for pediatric PEComa of the colon.
