Uncommon of the Uncommon: Malignant Perivascular Epithelioid Cell Tumor of the Lung.
10.3348/kjr.2013.14.4.692
- Author:
Hyun Ju LIM
1
;
Ho Yun LEE
;
Joungho HAN
;
Yong Soo CHOI
;
Kyung Soo LEE
Author Information
1. Department of Radiology and Center for Imaging, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul 135-710, Korea. hoyunlee96@gmail.com
- Publication Type:Case Reports
- Keywords:
Perivascular epithelioid cell;
Pecoma;
Clear cell sugar tumor;
Lung tumor
- MeSH:
Diagnosis, Differential;
Follow-Up Studies;
Humans;
Lung Neoplasms/*diagnosis/surgery;
Male;
Middle Aged;
Perivascular Epithelioid Cell Neoplasms/*diagnosis/surgery;
Pneumonectomy;
Positron-Emission Tomography/*methods;
Thoracic Surgery, Video-Assisted/methods;
Tomography, X-Ray Computed/*methods
- From:Korean Journal of Radiology
2013;14(4):692-696
- CountryRepublic of Korea
- Language:English
-
Abstract:
A perivascular epithelioid cell (PEC) tumor is a rare mesenchymal tumor characterized by abundant cytoplasmic Periodic acid-Schiff positive glycogen (also called sugar tumor or clear cell tumor of the lung for this characteristic) and is mostly benign. We report a case of a 63-year-old man who presented with an enlarging mass on chest radiograph. After a thorough workup, diagnosis of malignant pulmonary PEC tumor with lung to lung metastases was established. Herein, the difficulties of diagnosis and management we confronted are described.
