Mononeuritis Multiplex in Association with Anti-neutrophil Cytoplasmic Autoantibody(?) Vasculitis: A case report.
- Author:
Min Seok KIM
1
;
Hee Sang KIM
;
Chi Moon HWANG
;
Kyung Hoi AHN
Author Information
1. Department of Rehabilitation Medicine, Kyung Hee University College of Medicine, Korea.
- Publication Type:Case Report
- Keywords:
Mononeuritis multiplex;
Vasculitis;
Anti-neutrophil cytoplasmic autoantibody
- MeSH:
Angiography;
Anti-Neutrophil Cytoplasmic Antibody-Associated Vasculitis;
Antibodies, Antineutrophil Cytoplasmic;
Biopsy;
Cyclophosphamide;
Cytoplasm*;
Dyspnea;
Edema;
Female;
Glomerulonephritis;
Humans;
Lymphoma;
Middle Aged;
Mononeuropathies*;
Polyarteritis Nodosa;
Prednisolone;
Sarcoidosis;
Sural Nerve;
Systemic Vasculitis;
Vasculitis*;
Wegener Granulomatosis
- From:Journal of the Korean Academy of Rehabilitation Medicine
1997;21(5):1039-1044
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Mononeuritis multiplex may be a manifestation of systemic vasculitis or of other illnesses such as sarcoidosis, diabetes, lymphoma, and AIDS. Anti-neutrophil cytoplasmic autoantibody(ANCA) is a serologic marker for pauci-immune crescentic glomerulonephritis and systemic necrotizing arteritis, including polyarteritis nodosa, Wegener's granulomatosis and so-called ANCA-associated vasculitis. We report a case of mononeuritis multiplex due to ANCA associated vasculitis. A 46-year-old female visited hospital because of peripheral edema, pain and dyspnea. We diagnosed neuropathy associated with vasculitis by electrophysiologic study, sural nerve biopsy and angiography. The patient was treated with prednisolone and cyclophosphamide. Her symptoms and signs improved and her ANCA test was converted from positive to negative.