Juvenile Muscular Atrophy of the Upper Limb (Hirayama Disease): A case report.
- Author:
Hyun Kyung LEE
1
;
Dong Hyuk KIM
;
Pyeong Sik JEON
;
Sung Hoon LEE
;
Eun Young KANG
;
Se Jong KIM
Author Information
1. Department of Rehabilitation Medicine, Kwangju Christian Hospital, Korea. dirzahlee@hanmail.net
- Publication Type:Case Report
- Keywords:
Hirayama disease;
Focal amyotrophy;
Neck flexion
- MeSH:
Adolescent;
Humans;
Male;
Muscle Weakness;
Neck;
Spinal Muscular Atrophies of Childhood*;
Upper Extremity*
- From:Journal of the Korean Academy of Rehabilitation Medicine
2004;28(4):387-391
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Hirayama disease is characterized by focal amyotrophy of the upper limb associated with unilateral or asymmetric bilateral muscle weakness. It occurs in young men in their late teens or early twenties. Repeated or sustained neck flexion is thought to be a cause of the disease. It is important to prevent the progression of the disease through early recognition and management. We reported a patient with Hirayama disease in order to review the typical clinical, electrodiagnostic and radiological findings of Hirayama disease.
