Autosomal Dominant Polycystic Kidney Disease with an Asymptomatic Type I Choledochal Cyst.
- Author:
Seung Jee RYU
1
;
Kyung Hoon KIM
;
Tae Wan KIM
;
Woo Ho BAN
;
Su Lim LEE
;
Sung Soo KIM
;
Young Ok KIM
Author Information
1. Department of Internal Medicine, The Catholic University of Korea College of Medicine, Seoul, Korea. cmckyo@catholic.ac.kr
- Publication Type:Case Report
- Keywords:
ADPKD;
Choledochal cyst;
Polycystic liver disease
- MeSH:
Bile Ducts, Extrahepatic;
Cholangiopancreatography, Magnetic Resonance;
Choledochal Cyst;
Cysts;
Dilatation;
Female;
Humans;
Kidney;
Kidney Failure, Chronic;
Liver;
Liver Diseases;
Polycystic Kidney, Autosomal Dominant;
Reference Values
- From:Korean Journal of Medicine
2013;85(2):205-209
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Autosomal dominant polycystic kidney disease (ADPKD) is the most common inherited renal disease. Polycystic liver disease is commonly observed in ADPKD but rarely has it been associated with a choledochal cyst. We report a case of a choledochal cyst with ADPKD in a 60-year-old female patient with ADPKD and concomitant chronic renal failure who was admitted because of acute deterioration of kidney function due to poor oral intake. There was no history of a biliary disorder and her kidney function recovered promptly after fluid replacement. Non-enhanced computed tomography was performed to evaluate ADPKD and revealed numerous cysts in both kidneys and liver. It also showed fusiform dilatation of the extrahepatic bile ducts, a finding indicative of a choledochal cyst. Liver function was within the normal range and there was no evidence of extrahepatic biliary obstruction. Magnetic resonance cholangiopancreatography confirmed the diagnosis of a type I choledochal cyst combined with ADPKD.
