A Case of Isolated Right Ventricular Hypoplasia without Tricuspid Atresia or Pulmonary Atresia.
- Author:
Eui Jun YANG
1
;
Sun Young KIM
;
Sank Ook NAM
;
Hee Ju PARK
;
Nam Hee KWAK
Author Information
1. Department of Pediatrics, College of Medicine, Pusan National University, Pusan, Korea.
- Publication Type:Case Report
- Keywords:
Isolated right ventricular hypoplasia;
Congenital heart disease
- MeSH:
Cyanosis;
Diagnosis;
Foramen Ovale, Patent;
Heart Defects, Congenital;
Heart Septal Defects, Atrial;
Heart Ventricles;
Humans;
Infant, Newborn;
Pulmonary Atresia*;
Tricuspid Atresia*;
United Nations
- From:Journal of the Korean Pediatric Society
1999;42(7):1026-1030
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Isolated right ventricular hypoplasia, unassociated with severe pulmonary or tricuspid valvar malformations, is a rare primary congenital cardiac anomaly in which of the trabecular portion of right ventricle fails to develop. An atrial septal defect or a patent foramen ovale serves as an escape valve. We observed a 2-day-old neonate with this disorder who suffered from cyanosis. The diagnosis was made by Doppler-echocardiography which revealed marked reduction in right ventricular size and right-to-left shunt through the atrial septal defect. There was no other cardiac malformation such as pulmonary atresia or tricuspid atresia.
