MSCT manifestations of hepatic fat-poor perivascular epithelioid cell tumor
10.3969/j.issn.1002-1671.2018.06.022
- VernacularTitle:肝脏乏脂肪型血管周上皮样细胞肿瘤的MSCT表现
- Author:
Yaqiong HE
1
;
Jingjiang YAO
;
Jianbin LIU
;
Hongling LI
Author Information
1. 湖南省人民医院放射科
- Keywords:
liver neoplasms;
perivascular epithelioid cell tumor;
computed tomography
- From:
Journal of Practical Radiology
2018;34(6):901-904
- CountryChina
- Language:Chinese
-
Abstract:
Objective To investigate the MSCT manifestations of hepatic fat-poor perivascular epithelioid cell tumor (PEComa). Methods CT and pathological findings of 8 patients with hepatic fat-poor PEComa confirmed by surgery were assessed retrospectively.Results 8 cases had solitary lesion,all lesions with round or round-like shape.The largest diameter ranged 20-110 mm.The fat density was not measured by CT scan.6 lesions composed of solid component,and solid part showed obviously enhancement on arterial phase.On portal venous phase and parenchymal phase,the tumors showed equal or low or slightly high density.2 lesions showed cystic necrosis,peripheral enhancement on arterial phase,1 lesion showed continuous enhancement and the enhancement degree increased,and another lesion showed reduced enhancement.All lesions had tortuous vascular in the center of lesions or at the peripheral.Immunohistochemistry examinations showed that HMB45,Melan-A and SMA were positive in all cases,CD31,CD34 and S-100 expressed positive in partial cases. Conclusion The CT findings of hepatic fat-poor PEComa are lack of specificity.When the enhancement and clearance pattern of liver mass is similar to hepatocellular carcinoma or adenoma,the clinical history does not support the diagnosis,may consider the possibility of PEComa when tortuous vascular in the center of lesions or at the peripheral on arterial phase.
