Diagnosis and differential diagnosis of infantile cholestasis disease
10.3760/cma.j.issn.2095-428X.2018.19.001
- VernacularTitle:婴儿胆汁淤积性肝病的诊断及鉴别诊断
- Author:
Chen DONG
1
;
Zhihua HUANG
Author Information
1. 华中科技大学同济医学院附属同济医院儿科学系
- Keywords:
Cholestasis;
Jaundice;
Biliary atresia;
Infant;
newborn
- From:
Chinese Journal of Applied Clinical Pediatrics
2018;33(19):1441-1447
- CountryChina
- Language:Chinese
-
Abstract:
Infantile cholestasis disease is a common liver disease in infancy (including neonatal period). It is caused by intra - or extrahepatic factors. First of all,a differential diagnosis of biliary atresia and non - biliary atresia intrahepatic cholestasis needs to be made. The diagnosis should be made according to clinical manifestation,laboratory test results,imaging results and liver pathology. Numerous etiologies can cause intrahepatic cholestasis. Genetic factors are research focus now. Therapy on the etiologies is an effective therapeutic measure.