Research progress of Kaposiform hemangioendothelioma
10.3760/cma.j.issn.2095-428X.2018.11.023
- VernacularTitle:卡波西样血管内皮瘤研究进展
- Author:
Yuanfang ZHANG
1
;
Changxian DONG
Author Information
1. 河南省人民医院血管瘤外科
- Keywords:
Kaposiform hemangioendothelioma;
Kasabach Meritt phenomenon;
Hemangioma;
Thrombocytopenia
- From:
Chinese Journal of Applied Clinical Pediatrics
2018;33(11):874-877
- CountryChina
- Language:Chinese
-
Abstract:
Kaposiform hemangioendothelioma(KHE) is a kind of organization form is similar to Kaposi's sarcoma(KS) and aggressive cancer,found in children and infants are rare and multiple in the limbs,torso,facial skin and deep soft tissue can also occur in the mediastinum,retroperitoneal etc.KHE is one of the main causes of Kasabach Meritt phenomenon(KMP) in infants and young children,the mortality rate is as high as 10％-37％,even 52％.At present,there is no uniform and effective treatment method at home and abroad.The clinical manifestations,diagnosis and treatment of KHE are reviewed.
