Primary intestinal lymphangiectasia in children
10.3760/cma.j.issn.2095-428X.2018.07.003
- VernacularTitle:儿童原发小肠淋巴管扩张症
- Author:
Huiqing SHEN
1
Author Information
1. 100045 国家儿童医学中心,首都医科大学附属北京儿童医院消化科,首都医科大学消化病学系,国家消化系统疾病临床医学研究中心
- Keywords:
Lymphangiectasis;
Intestinal;
Lymphatic radionuclide imaging;
Child
- From:
Chinese Journal of Applied Clinical Pediatrics
2018;33(7):490-495
- CountryChina
- Language:Chinese
-
Abstract:
With the progress of clinical understanding and examination methods,the incidence of primary intestinal lymphangiectasia in children is gradually increased,congenital lymphatic malformation is the most common pathogen,protein-losing enteropathy is the main clinical feature.In addition to endoscopic and histologic examination,lymphatic radionuclide imaging,has become the common method in diagnosis,especially suitable for infants and young children.The management of lymphangiectasia include:a low-fat diet associated with supplementary medium chain three acyl glycerol,symptomatic treatment,medicine and surgery.Emphasis should be put on long-term management and follow-up work.
