Pulmonary veno-occlusive disease/pulmonary capillary hemangiomatosis: A case report and literature review
10.11817/j.issn.1672-7347.2018.05.017
- VernacularTitle:肺静脉闭塞病/肺毛细血管瘤样病Ⅰ例及文献复习
- Author:
Xianliang XIONG
1
;
Tengteng ZHU
;
Jiang LI
Author Information
1. 中南大学湘雅二医院心内科
- Keywords:
pulmonary veno-occlusive disease;
pulmonary capillary hemangiomatosis;
pulmonary arterial hypertension
- From:
Journal of Central South University(Medical Sciences)
2018;43(5):571-576
- CountryChina
- Language:Chinese
-
Abstract:
Pulmonary veno-occlusive disease (PVOD)/pulmonary capillary hemangiomatosis (PCH) is a rare form of pulmonary vascular disease that causes pulmonary arterial hypertension.The diagnosis of PVOD/PCH can be established by the combination of clinical features,physical examination,radiological findings,lung function,bronchoscopy and other resources.There is no established medical therapy for PVOD/PCH,and the only curative therapy for PVOD/PCH is lung transplantation.A girl with PVOD/PCH was diagnosed in the Second Xiangya Hospital.Combining the characteristics for this case with the relevant literature,we summarized the epidemiology,etiology,diagnosis and treatment for the disease to raise doctors' awareness for this rare disease.
