Malignant Rhabdoid Tumor of Kidney in Infant.
- Author:
Dong Gil SHIN
1
;
Sang Don LEE
;
Young Tak LIM
;
Chang Hun LEE
Author Information
1. Department of Urology, Dae Dong Hospital, Korea.
- Publication Type:Case Report
- Keywords:
Rhabdoid tumor;
Kidney
- MeSH:
Biopsy;
Chemotherapy, Adjuvant;
Child;
Female;
Humans;
Infant*;
Kidney*;
Liver;
Lung;
Lymph Nodes;
Neoplasm Metastasis;
Nephrectomy;
Rhabdoid Tumor*;
Wilms Tumor
- From:Korean Journal of Urology
2003;44(4):386-389
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
A malignant rhabdoid tumor of the kidney, an uncommon renal tumor of children, is one of the most lethal neoplasms in early life. It was considered to be a sarcomatous variant of Wilms' tumor; however, further studies of its histological and clinical characteristics have proven it to be a distinct entity. We report a case of malignant rhabdoid tumor of the kidney in a 3-month-old girl, with a left abdominal palpable mass that had developed over the previous month. A left radical nephrectomy, with a regional lymph node biopsy, and 4 cycles of adjuvant chemotherapy, was performed. On the 45th postoperative day, multiple metastasises in liver, contralateral kidney and left upper lobe of lung were found. The patient expired 2 months after the operation.
