A case of Sweet syndrome involving small bowel.
- Author:
Mira KANG
1
;
Eun Ha PARK
;
Hyun Wook JUNG
;
Kee Taek JANG
;
Won Sup OH
;
Kyong Ran PECK
;
Jae Hoon SONG
Author Information
1. Department of Medicine, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul, Korea. wsoh@smc.samsung.co.kr
- Publication Type:Case Report
- Keywords:
Sweet syndrome;
Intestines;
Myelodysplastic syndrome
- MeSH:
Abdominal Pain;
Adrenal Cortex Hormones;
Biopsy;
Bone Marrow;
Fever;
Humans;
Intestines;
Laparotomy;
Leg;
Lower Extremity;
Male;
Middle Aged;
Myelodysplastic Syndromes;
Neutrophils;
Pancytopenia;
Skin;
Sweet Syndrome*;
Tomography, X-Ray Computed
- From:Korean Journal of Medicine
2004;67(Suppl 3):S809-S813
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Sweet syndrome is characterized by fever and abrupt appearance of painful, erythematous plaques: a dermal infiltrate of mature neutrophils. Extracutaneous manifestations often occur in Sweet syndrome, but intestinal involvement is extremely rare. We report a case of Sweet syndrome involving small bowel in a 56-year old male with fever and abdominal pain. An abdominal CT showed diffuse wall thickening in the ileal loop. He underwent explorative laparotomy and segmental resection of involved small bowel. Skin, bone marrow, and muscle biopsies were done because he had persistent fever, cutaneous plaques, pancytopenia, and swelling of lower extremities after operation. Finally, he was diagnosed as myelodysplastic syndrome combined with Sweet syndrome, which involved small bowel, skin, and muscle simultaneously. Fever, cutaneous plaques and leg swelling resolved after systemic administration of corticosteroids.
