Mesectodermal Leiomyosarcoma :A Case Report.
- Author:
Seong Heon MOON
1
;
Kyung In WOO
;
Yoon Duck KIM
;
Yeon Lim SUH
Author Information
1. Department of Ophthalmology, Samsung Medical Center, School of Medicine, Sungkyunkwan University.
- Publication Type:Case Report
- Keywords:
Mesectodermal leiomyosarcoma;
Orbital tumor;
Proptosis
- MeSH:
Aged, 80 and over;
Biopsy;
Diagnosis;
Exophthalmos;
Female;
Humans;
Korea;
Leiomyosarcoma*;
Myocytes, Smooth Muscle;
Orbit;
Rare Diseases
- From:Journal of the Korean Ophthalmological Society
2000;41(3):777-783
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
The mesectodermal leiomyosarcoma of the orbit is extremely rare disease. An 81-year-old woman presented with progressive painless proptosis in her right eye of 1 month duration. Computed tomographic scan of the orbit demonstrated 5-cm size lobulating mass of the right orbit which displaces eyeball anteriorly and bulges out to temporalis portion with severe destruction of lateral orbital wall and intracranial extension. For diagnostic pur-pose, incisional biopsy was performed. Light microscopic examination showed the characteristics of neurogenic tumor. Electron microscopic examination disclosed the features of smooth muscle cells as well as neural differentiation of the tumor, leading to the diagnosis of mesectodermal leiomyosarcoma. To the best of our knowledge, this is the first case of mesectodermal leiomyosar-coma of the orbit in Korea
