A Case of Neonatal Cholestasis Associated with Congenital Adrenal Hyperplasia.
- Author:
Seon Yun CHOI
1
;
Jun Chul BYUN
;
Won Joung CHOI
;
Heung Sik KIM
;
Una KANG
;
Jin Bok HWANG
Author Information
1. Department of Pediatrics, Keimyung University School of Medicine, Daegu, Korea. pedgi@korea.com
- Publication Type:Case Report
- Keywords:
Neonatal cholestasis;
Congenital adrenal hyperplasia
- MeSH:
Adrenal Hyperplasia, Congenital*;
Bile;
Cholestasis*;
Hydrocortisone;
Hypopituitarism
- From:Korean Journal of Pediatric Gastroenterology and Nutrition
2005;8(1):87-90
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
It has been suggested that cortisol deficiency may be responsible for the cholestasis. Although congenital hypopituitarism was reported as a possible cause of neonatal cholestasis, congenital adrenal hyperplasia with neonatal cholestasis is a very rare report in the literature. We experienced a case presenting with neonatal cholestasis associated with congenital adrenal hyperplasia. This case provides a clinical evidence supporting the notion that cortisol has an important physiological role in bile acid synthesis and transport.
