Congenital Herditary Stromal Dystrophy of the Cornea.
- Author:
Si Il RYU
1
;
Hyung Jun KIM
;
Jyung Sik KWAK
Author Information
1. Department of Ophthalmology, Daegu Catholic Hospital, Korea.
- Publication Type:Original Article
- Keywords:
congenital hereditary stromal dystrophy;
stromal fibrogenesis
- MeSH:
Cornea*;
Humans
- From:Journal of the Korean Ophthalmological Society
1991;32(1):1-8
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
In 1978, a nonprogressive corneal dystrophy was seperated from other causes of congenital opacification on the basis of unique clinincal findings and characteristic electronmicroscopic findings. This disorder, termed congenital hereditary stromal dystrophy, appears to the result of disordered stromal fibrogenesis. Recently, the autors have experienced 4 members of a family with typical electronmicroscopic findings of congenital heaeditary stromal dystrophy of the cornea. In this report we describe the characteristic findings of congenital hereditary stromal dystrophy.
