A case of jejunal primitive neuroectodermal tumor in an adult female.
- Author:
Ki Hwan KIM
1
;
Ji Young RHEE
;
Jae Kyung LEE
;
Hwa Young CHO
;
Seock Ah IM
;
Kyu Joo PARK
;
Chong Jai KIM
Author Information
1. Department of Internal Medicine, Seoul National University College of Medicine, Seoul, Korea. moisa@snu.ac.kr
- Publication Type:Case Report
- Keywords:
Neuroectodermal Tumors;
Chemotherapy;
Jejunum
- MeSH:
Adolescent;
Adult;
Anorexia;
Child;
Doxorubicin;
Etoposide;
Extremities;
Female;
Gastrointestinal Tract;
Humans;
Ifosfamide;
Jejunum;
Nausea;
Neuroectodermal Tumors;
Neuroectodermal Tumors, Primitive;
Sarcoma, Ewing;
Vincristine;
Vomiting;
Weight Loss
- From:Korean Journal of Medicine
2008;75(2):237-241
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Primitive neuroectodermal tumor (PNET) is frequent in children and adolescents, but rare in adults. Most of the extraosseous Ewing's sarcoma or PNET occur in the soft tissues of the extremities, the paravertebral region, and the pelvic cavity. PNET in the gastrointestinal tract is uncommon. We report herein a case of PNET arising from the jejunum in a 38-year-old woman. She presented with anorexia, nausea, vomiting, and weight loss. Abdominal computed tomography revealed a mass in the small bowel with obstruction. She had a small bowel segmental resection, from which PNET was diagnosed. Multi-agent chemotherapy comprised of vincristine, adriamycin, cyclophophamide, ifosfamide, and etoposide (VAC/IE) was administered for 1 year. The treatment was well-tolerated. She remains alive and continues to be disease free 30 months postoperatively.
