A Case of Malignant Atrophic Papulosis Showed Typical Skin and Intestinal Lesions.
- Author:
Jeong Soo KIM
1
;
Kyung Ho KIM
;
Min Su PARK
;
Ki Beom SHUR
;
Jeung Hoon LEE
;
Jang Kyu PARK
;
In Sang SONG
Author Information
1. Department of Dermatology, College of Medicine Chungnam National University, Taej on, Korea. seokb@cnu.ac.kr
- Publication Type:Case Report
- Keywords:
Malignant atrophic papulosis
- MeSH:
Adult;
Body Surface Area;
Cicatrix;
Dermis;
Dipyridamole;
Epidermis;
Humans;
Intestinal Perforation;
Intestine, Large;
Laparotomy;
Male;
Malignant Atrophic Papulosis*;
Mucins;
Necrosis;
Respiratory Insufficiency;
Respiratory System;
Salicylic Acid;
Skin*
- From:Korean Journal of Dermatology
2002;40(1):48-53
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
A 33-year-old male patient had malignant atrophic papulosis that affected the skin and intestinal tract and probably respiratory system. He had multiple typical skin lesion with porcelain-white atrophic scars on the whole body surface area except on face, palm and sole. And he had been operated two times due to intestinal perforation after onset. Multiple whitish necrotic patches were found in small and large intestine during laparotomy. Also he had a plueral effusion. Histopathologic studies showed atrophic epidermis and dermal necrosis, vascular change, mucin deposition in lower dermis. He was treated with acetyl salicylic acid and dipyridamole, but there was no improve-ment. He died of intestinal perforation and respiratory failure 67 months after onset(6 months after onset of abdominal symptom).