Motor Axonal Neuropathy Associated With Idiopathic CD4+ T-Lymphocytopenia.
10.5535/arm.2013.37.1.127
- Author:
Tae Im YI
1
;
Bo Ra KIM
;
In Soo HAN
;
Bo Kyoung KIM
Author Information
1. Department of Rehabilitation Medicine, Daejin Medical Center Bundang Jesaeng General Hospital, Seongnam, Korea. 007bora@hanmail.net
- Publication Type:Case Report
- Keywords:
Axonal neuropathy;
Idiopathic CD4-positive T-lymphocytopenia
- MeSH:
Axons;
Diagnosis, Differential;
Electromyography;
Extremities;
Humans;
Immune System Diseases;
Lymphopenia;
Needles;
Neural Conduction;
Opportunistic Infections;
T-Lymphocytes;
T-Lymphocytopenia, Idiopathic CD4-Positive
- From:Annals of Rehabilitation Medicine
2013;37(1):127-132
- CountryRepublic of Korea
- Language:English
-
Abstract:
Idiopathic CD4+ T-lymphocytopenia is a rare immune disorder characterized by an unexplained deficit of CD4+ T cells and results in various opportunistic infections. Herein, we report a case of new onset weakness in a 10-year-old boy secondary to motor axonal neuropathy associated with idiopathic CD4+ T-lymphocytopenia. The patient was referred to rehabilitation for an evaluation of progressive weakness involving all four limbs. A subsequent nerve conduction study and needle electromyography identified motor axonal neuropathy. At that time, laboratory studies specific to the differential diagnosis of motor axonal neuropathy were performed; however, the abnormality noted was a decreased CD4+ T-lymphocyte count. Motor axonal neuropathy represents an uncommon manifestation of idiopathic CD4+ T-lymphocytopenia and is probably associated with an underlying immune process.
