Clinical and echocardiographic characteristics of cardiac papillary fibroelastoma in adults
10.13929/j.1003-3289.201704121
- VernacularTitle:成人心脏乳头状弹力纤维瘤的临床和超声心动图特征
- Author:
Jiancheng HAN
1
;
Fei TENG
;
Xu YANG
;
Lin SUN
;
Xiaoyan GU
;
Ye ZHANG
;
Ying ZHAO
;
Shuang GAO
;
Yihua HE
Author Information
1. 首都医科大学附属北京安贞医院超声科
- Keywords:
Heart neoplasms;
Papillary fibroelastoma;
Echocardiography
- From:
Chinese Journal of Medical Imaging Technology
2017;33(10):1497-1500
- CountryChina
- Language:Chinese
-
Abstract:
Objective To explore the clinical features and echocardiographic characteristics of cardiac papillary fibroelastoma (CPF) in adults.Methods Clinical features,echocardiographic characteristics,surgical procedures and outcomes were retrospectively evaluated in 13 patients with CPF confirmed by pathology.Results The clinical features of CPF were atypical.The most common symptoms were chest distress and short breath.All the 13 patients were single lesions,9 cases (9/13,69.23％) involved the valves (4 on the aortic valve,3 on the mitral valve,2 on the tricuspid valve) and 4 cases (4/13,30.77％) involved the chambers (2 in the right atrium,1 in the right ventricle,1 in the left ventricle).The largest diameters of ＞2 mm were in 8 cases and ≤2 mm were in 5 cases.Eight cases were detected by echocardiographic examination and 5 cases were missed.Surgical excision was performed in 8 patients and prosthetic valve replacement was performed in 5 patients.Conclusion The clinical symptoms of CPF are variable.When the size of CPF is too small,echocardiography is difficult to detect.Most of CPFs originate on the valves,predominantly on the aortic valve.The prognosis of CPF is excellent.
