A Narrow Internal Auditory Canal with Duplication in a Patient with Congenital Sensorineural Hearing Loss.

Author: Hye Won BAIK ¹ ; Hyeon YU ; Kyung Soo KIM ; Gi Hyeon KIM
Author Information

1. Department of Radiology, Chung-Ang University Hospital, College of Medicine, Chung-Ang University, Seoul, Korea. hyeonyu@cau.ac.kr
Publication Type:Case Report ; Research Support, Non-U.S. Gov't
Keywords: Ear, abnormalities; Ear anatomy; Ear, MR; Magnetic resonance (MR), pulse sequences; Magnetic resonance (MR), thin section; Nerves, abnormalities
MeSH: Child; Ear, Inner/*abnormalities/radiography; Female; Hearing Loss, Sensorineural/*congenital; Humans; Tomography, X-Ray Computed
From:Korean Journal of Radiology 2008;9(Suppl):S22-S25
CountryRepublic of Korea
Language:English
Abstract: A narrow internal auditory canal (IAC) with duplication is a rare anomaly of the temporal bone. It is associated with congenital sensorineural hearing loss. Aplasia or hypoplasia of the vestibulocochlear nerve may cause the hearing loss. We present an unusual case of an isolated narrow IAC with duplication that was detected by a CT scan. In this case, the IAC was divided by a bony septum into an empty stenotic inferoposterior portion and a large anterosuperior portion containing the facial nerve that was clearly delineated on MRI.