Congenital Middle Ear Cholesteatoma in Children.
- Author:
Jong Hyung KIM
1
;
Kyung Ho PARK
;
Shi Nae PARK
;
Jun Ook PARK
;
Sung Jin HONG
;
Ji Young CHOI
;
Sang Won YEO
Author Information
1. Department of Otolaryngology-HNS, College of Medicine, The Catholic University of Korea, Seoul, Korea. swyeo@catholic.ac.kr
- Publication Type:Original Article
- Keywords:
Children;
Congenital middle ear cholesteatoma;
Temporal bone CT
- MeSH:
Adolescent;
Child*;
Cholesteatoma;
Cholesteatoma, Middle Ear*;
CME-Carbodiimide;
Ear, Middle*;
Hearing;
Humans;
Outcome Assessment (Health Care);
Pathology;
Recurrence;
Retrospective Studies;
Tomography, X-Ray Computed
- From:Korean Journal of Otolaryngology - Head and Neck Surgery
2006;49(7):682-687
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
BACKGROUND AND OBJECTIVES: Congenital middle ear cholesteatoma (CMEC) is a rare entity that may go undiagnosed for years. Aims of this study were to assess the characteristic features and recurrence of CMEC in pediatric patients of different stages and to determine the value of preoperative CT scan in CMEC. SUBJECTS AND METHOD: Thirty cases of CMEC under 15 years old that had been treated at the hospitals of the Catholic University from 1995 through 2005 were reviewed retrospectively. The age range was from 2 to 13 with the mean age of 6.2. The main outcome measures were CT findings, surgical findings, recurrence rate and hearing assessment. RESULTS: Preoperative CT scan accurately predicted the extent of the cholesteatoma seen during surgery in 25/30 (83.3%). The recurrence rate of CMEC was 6.7% (2/30) and all of recurrent cases were belonged to stage IV. In the recurrent cases, cholesteatomas were extended to sinus tympani and facial recess at revisional operation as well as at the initial operation. CONCLUSION: Preoperative CT scan is essential in defining the extent of existing pathology. The intra-operative CMEC extension and location influence the outcome of surgery. In the higher stages, careful eradication of disease, particularly in the region of sinus tympani and facial recess, are recommended.
