Pneumonectomy Case in a Newborn with Congenital Pulmonary Lymphangiectasia.
10.3346/jkms.2014.29.4.609
- Author:
Joon Ho HWANG
1
;
Joo Heon KIM
;
Jung Ju HWANG
;
Kyu Soon KIM
;
Seung Yeon KIM
Author Information
1. Department of Pediatrics, Eulji University College of Medicine, Daejeon, Korea. dunggiduk@eulji.ac.kr
- Publication Type:Case Reports
- Keywords:
Lymphangiectasia, Pulmonary, Congenital;
Infant, Newborn;
Pneumonectomy
- MeSH:
Female;
Gestational Age;
Humans;
Infant, Newborn;
Lung/pathology;
Lung Diseases/*congenital/diagnosis/pathology/radiography;
Lymphangiectasis/*congenital/diagnosis/pathology/radiography;
Lymphatic Vessels/pathology;
Tomography, X-Ray Computed
- From:Journal of Korean Medical Science
2014;29(4):609-613
- CountryRepublic of Korea
- Language:English
-
Abstract:
Congenital pulmonary lymphangiectasia (CPL) is a rare lymphatic pulmonary abnormality. CPL with respiratory distress has a poor prognosis, and is frequently fatal in neonates. We report a case of pneumonectomy for CPL in a newborn. An infant girl, born at 39 weeks' after an uncomplicated pregnancy, exhibited respiratory distress 1 hr after birth, which necessitated intubation and aggressive ventilator care. Right pneumonectomy was performed after her symptoms worsened. Histologic examination indicated CPL. She is currently 12 months old and developing normally. Pneumonectomy can be considered for treating respiratory symptoms for improving chances of survival in cases with unilateral CPL.
