A Case of Histiocytic Sarcoma Arising in Head and Neck Region with Rhabdoid Differentiation.
10.3342/kjorl-hns.2016.59.9.672
- Author:
Jeong Marn KIM
1
;
Yun Seok OH
;
Dong Wook LEE
Author Information
1. Department of Otorhinolaryngology-Head and Neck Surgery, College of Medicine, Chungbuk National University, Cheongju, Korea. dwlee@chungbuk.ac.kr
- Publication Type:Case Report
- Keywords:
Head and neck sarcoma;
Histiocytic sarcoma;
Rhabdoid differentiation
- MeSH:
B-Lymphocytes;
Head*;
Hematologic Neoplasms;
Histiocytes;
Histiocytic Sarcoma*;
Humans;
Middle Aged;
Neck*;
Sarcoma
- From:Korean Journal of Otolaryngology - Head and Neck Surgery
2016;59(9):672-675
- CountryRepublic of Korea
- Language:English
-
Abstract:
Head and neck sarcomas account for about 1% of malignant head and neck tumors, and histiocytic sarcomas (HSs) account for less than 1% of all hematolymphoid neoplasms. These rare hematopoietic neoplasms are the result of a malignant proliferation of cells. They have morphological and immunophenotypic features of mature tissue histiocytes, which play a major role in processing and presenting antigens to T or B lymphocytes. The mesenchymal differentiation of HSs has not been reported. We describe a case of HS with rhabdoid differentiation in a 55-year-old man who presented with a 3×2.5×2 cm mass in the left supraclavicular area. To the best of our knowledge, this is the first report worldwide of a primary HS with rhabdoid differentiation.
