A Case of Spontaneous Neck Bleeding in Neurofibromatosis Type I.
- Author:
Jong Sun LEE
1
;
Hyung Ro CHU
;
Jong Bum YOO
;
Chong Woo YOO
Author Information
1. Department of Otorhiolaryngology-Head and Neck Surgery, Hallym University College of Medicine, Seoul, Korea.
- Publication Type:Case Report
- Keywords:
Neurofibromatosis;
Neck;
Bleeding
- MeSH:
Acoustics;
Cafe-au-Lait Spots;
Emergencies;
Hemorrhage*;
Humans;
Neck*;
Neurofibroma;
Neurofibromatoses*;
Neurofibromatosis 1*
- From:Korean Journal of Otolaryngology - Head and Neck Surgery
2006;49(5):579-582
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
It is rare to find spontaneous cervical bleedings for which a wide variety of etiologies have been reported. We experienced a case of spontaneous cervical bleeding that caused emergency operation. We present this case with a review of the literature. This case demonstrates a potentially lethal complication in patients with neurofibroma. Neurofibroma is an inherited disease, classified as 'classical (type I, von Recklinghausen, multiple or peripheral neurofibromatosis)', 'central (type II, bilateral acoustic neurofibromatosis)' and other types. The pathognomic features of classical neurofibromatosis are cafe-au-lait spots and neurofibromas. Other clinical features are variably expressed and occurnece of severe hemorrhage is an unusual complication. Conservative management do not stop the hemorrhage. Surgical exploration must be undertaken for cure.
