Two Cases of Enlarged Vestibular Aqueduct Syndrome.
- Author:
Joong Keun KWON
1
;
Si Hyung KIM
;
Seung Moon BAEK
;
Jung Kueon NAM
Author Information
1. Department of Otolaryngology-Head and Neck Surgery, Ulsan University College of Medicine, Ulsan, Korea. kwonmail@hanafos.com
- Publication Type:Case Report
- Keywords:
Enlarged vestibular aqueduct syndrome (EVAS);
Endolymphatic sac;
MRI
- MeSH:
Bone Conduction;
Ear;
Endolymphatic Duct;
Endolymphatic Sac;
Hearing Loss;
Humans;
Magnetic Resonance Imaging;
Temporal Bone;
Vestibular Aqueduct*
- From:Korean Journal of Otolaryngology - Head and Neck Surgery
2004;47(8):787-790
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
A large vestibular aqueduct, an isolated anomaly of temporal bone, is relatively rare and its association with sensorinerual hearing loss in childhood is known as the enlarged vestibular aqueduct syndrome. Using MRI, we found enlarged endolymphatic ducts and sacs in four ears of our two patients. Signal intensity of enlarged endolymphatic sac that is detected higher than that of CSF in Fluid Attenuated Inversion Recovery (FLAIR) image may indicate poor prognisis with respect to bone conduction threshold in pure tone audiogram.
