A Case of Laryngeal Rhabdomyoma.
- Author:
Phil Sang CHUNG
1
;
Young Hoon KIM
;
Na Hye MYONG
Author Information
1. Department of Otolaryngology-Head and Neck Surgery, College of Medicine, Dankook University, Cheonan, Korea.
- Publication Type:Case Report
- Keywords:
Rhabdomyoma;
Larynx;
Adult type
- MeSH:
Adult;
Diagnosis;
Diagnosis, Differential;
Head;
Heart;
Humans;
Korea;
Larynx;
Microscopy, Electron;
Mouth;
Nasopharynx;
Neck;
Orbit;
Pharynx;
Rhabdomyoma*
- From:Korean Journal of Otolaryngology - Head and Neck Surgery
1997;40(1):126-130
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Rhabdomyoma have been found in many areas of the body, though most commonly in the heart. The extracardiac appearance of rhabdomyoma is unusual and the head and neck area is involved most commonly. Affected sites have included the larynx, pharynx, oral cavity, neck, nasopharynx and orbit. Particularly, the larynx is an uncommon site. This neoplasms in the larynx have been reported only 23 cases in the literature so far and not reported in Korea. The diagnosis was based on routine histological and immunohistological staining, and electron microscopy. The extracardiac rhabdomyoma was divided into three types according to histopathological findings: adult, fetal cellular and fetal myxoid type. The differential diagnosis and requisite diagnostic procedure are discussed. The treatment of choice is surgical excision. Recently, we have experienced a rhabdomyoma of the larynx, so we report with a review of literatures.