Nesidioblastosis with Hyperinsulinemic Hypoglycemia in Adult.
- Author:
Young Bin LEE
1
;
Chul Nam KIM
;
Tae Gil HUR
;
Gi Hong KIM
;
Myoung Soo LEE
;
Surg Hyo CHANG
Author Information
1. Department of General Surgery, Ilsan Paik Hospital, Inje University, Ilsan, Korea. cnkim@ilsanpaik.ac.kr
- Publication Type:Case Report
- Keywords:
Nesidioblastosis;
Hyperinsulinemic Hypoglycemia
- MeSH:
Adult*;
Angiography;
Calcium;
Endosonography;
Epithelium;
Fasting;
Humans;
Hypoglycemia*;
Middle Aged;
Nesidioblastosis*;
Pancreas;
Pancreatectomy;
Pancreatic Ducts;
Pathology
- From:Korean Journal of Hepato-Biliary-Pancreatic Surgery
2004;8(3):202-205
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Nesidioblastosis is a term that describes the prolonged differentiation of islets of Langerhan's cells from the epithelium of the pancreatic duct. Nesidioblastosis is a primarily childhood disease, which is often associated with hyperinsulinemic hypoglycemia, but rarely found in adults. A 62-year-old man with hyperinsulinemic hypoglycemia complained of general weakness and mental change while fasting. Abdominopelvic CT, celiac angiography, intra-arterial calcium stimulation test and endoscopic ultrasonography did not reveal any tumor in the pancreas. A subtotal pancreatectomy (nearly 80% of pancreas was removed) was then carried out. He was diagnosed with nesidioblastosis inform the pathology after the operation. Herein, our experience of a 62-year-old Nesidioblastosis patient is reported.