Nevoid Basal Cell Carcinoma Syndrome: A Case Report and Literature Review.
- Author:
Byung Kwon LEE
1
;
Jae Soo LEE
;
Dong Sik CHANG
;
Kyung Yu PARK
Author Information
1. Department of Otorhinolaryngology-Head and Neck Surgery, Eul-Ji University College of Medicine, Daejeon, Korea. otalgia@naver.com
- Publication Type:Case Report
- Keywords:
Nevoid basal cell carcinoma syndrome;
Odontogenic keratocyst
- MeSH:
Basal Cell Nevus Syndrome*;
Carcinoma, Basal Cell;
Cheek;
Keratosis;
Odontogenic Cysts;
Wills
- From:Korean Journal of Otolaryngology - Head and Neck Surgery
2005;48(6):819-822
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Nevoid basal cell carcinoma syndrome (NBCCS), also known as Gorlin-Goltz syndrome, shows autosomal dominant pattern of inheritance with variable expressivity. The most important features are the occurrence of basal cell carcinoma and odontogenic keratosis. Recently, we experienced a case of nevoid basal cell carcinoma syndrome with multiple odontogenic keratocysts, basal cell carcinoma on cheek, cerebral calcification and palmar pits. We report this case with literature review.
