Decompression of Internal Auditory Canal via Middle Fossa Approach in Neurofibromatosis Type II with Only Hearing Ear.
- Author:
Ju Wan KANG
1
;
Joong Wook SHIN
;
Won Sang LEE
;
Ho Ki LEE
Author Information
1. Department of Otorhinolaryngology, Yonsei University College of Medicine, Seoul, Korea. hokilee@yumc.yonsei.ac.kr
- Publication Type:Case Report
- Keywords:
Neurofibromatosis 2;
Acoustic neuroma;
Decompression surgical
- MeSH:
Central Nervous System;
Cranial Fossa, Middle;
Decompression*;
Ear*;
Hearing Loss;
Hearing*;
Humans;
Neurofibromatoses*;
Neurofibromatosis 2*;
Neuroma, Acoustic
- From:Korean Journal of Otolaryngology - Head and Neck Surgery
2006;49(4):439-442
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Neurofibromatosis type II (NF2) is a genetic disease and is transmitted as an autosomal dominant trait. NF2 is characterized by bilateral acoustic neuroma with multiple tumors of central nervous system. Progressive hearing loss is a significant problem in patients with NF2, and hearing preservation is an important factor for choice of treatment plan, especially in a NF2 patient with only one hearing ear. We report an experience of preservation of hearing in a NF2 patient with only one hearing ear through decompression of the internal auditory canal via middle cranial fossa approach.
