Hereditary Angioneurotic Edema of the Larynx: A Case Report and Literature Review.
- Author:
Dae Bo SHIM
1
;
Young Chang LIM
;
Hyang Ae SHIN
;
Jin Kook KIM
Author Information
1. Department of Otorhinolaryngology-Head and Neck Surgery, College of Medicine, Konkuk University, Seoul, Korea. entalk@kuh.ac.kr
- Publication Type:Case Report
- Keywords:
Angioneurotic edema;
Hereditary;
Larynx;
Treatment
- MeSH:
Adult;
Airway Obstruction;
Angioedema;
Angioedemas, Hereditary*;
Female;
Hereditary Angioedema Types I and II;
Humans;
Larynx*
- From:Korean Journal of Otolaryngology - Head and Neck Surgery
2006;49(4):464-467
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
Hereditary angioneurotic edema (HAE) is an autosomal dominant disease that results from the deficiency of C1 esterase inhibitor (C1-INH) function. Urgent proper intervention of the upper airway is warranted to save the life of patients with the disease, which often causes acute airway obstruction. We present, with a review of literature, a case of 37-year old woman with HAE of larynx.
