Interdisciplinary treatment for ectodermal dysplasia.
- Author:
Jin Hee KIM
1
;
Young Ku HOE
;
Jang Kyun OH
Author Information
1. Department of Orthodontics, Catholic Medical Center, Catholic University of Korea. kjhortho@cmc.cuk.ac.kr
- Publication Type:Original Article
- Keywords:
ectodermal dysplasia;
oligodontia;
interdisciplinary treatment;
loss of vertical dimension
- MeSH:
Anodontia;
Child;
Crowns;
Depression;
Ectoderm*;
Ectodermal Dysplasia*;
Eyebrows;
Fever;
Genetic Diseases, Inborn;
Hair;
Humans;
Male;
Mouth;
Skin;
Sweat Glands;
Vertical Dimension
- From:Korean Journal of Orthodontics
2000;30(6):739-745
- CountryRepublic of Korea
- Language:English
-
Abstract:
Ectodermal dysplasia is a hereditary disease characterized by a congenital dysplasia of one or more ectodermal structures. Characteristic manifestations include scanty hair and eyebrows, pigmented and hyperkeratinized skin around the eyes and mouth, frontal bossing with prominent supraorbital ridges, nasal bridge depression and dental anomalies. Hyperthermia or unexplained high fever as a result of the deficiency of sweat glands is common medical history. Findings of intraoral structures are anodontia or oligodontia with conical crowns. Consequently, generalized spacing and loss of vertical dimension of occlusion. Interdisciplinary approach has been performed to treat a 10-year old boy with ectodermal dysplasia. Orthodontists and a prosthodontist worked together on this case, and the result was satisfactory.
