Hemangioma of Endolymphatic Sac in Von Hippel-Lindau Patient.
10.3342/kjorl-hns.2015.58.10.729
- Author:
Yeo Jeen YI
1
;
Yewon KIM
;
Sung Hye PARK
;
Moo Kyun PARK
Author Information
1. Department of Otorhinolaryngology-Head & Neck Surgery, Seoul National University Hospital, Seoul National University College of Medicine, Seoul, Korea. aseptic@snu.ac.kr
- Publication Type:Case Report
- Keywords:
Endolymphatic sac tumor;
Hemangioma;
Sudden sensorineural hearing loss;
Von Hippel-Lindau disease
- MeSH:
Endolymphatic Sac*;
Hearing Loss, Sensorineural;
Hemangioma*;
Hemangioma, Capillary;
Humans;
Magnetic Resonance Imaging;
Male;
von Hippel-Lindau Disease;
Young Adult
- From:Korean Journal of Otolaryngology - Head and Neck Surgery
2015;58(10):729-733
- CountryRepublic of Korea
- Language:Korean
-
Abstract:
The present study reports a rare case of capillary hemangioma of endolymphatic sac. A 23-year-old male who underwent von Hippel-Lindau disease presented with recurrent sudden sensorineural hearing loss. Magnetic resonance imaging revealed a heterogenous enhanced mass in the right endolymphatic sac, which was hyperintense on the enhanced T1-weighted images and inhomogenous on the T2-weighted images. Pre-operatively, this tumor was believed to be an endolymphatic sac tumor because of the history of von Hippel-Lindau disease. During the surgery, vascular tumor was removed by transmastoid approach. A histopathological examination indicated that the tumor was a capillary hemangioma. To the best of our knowledge, the present study is the second case of hemangioma in the endolymphatic sac and first case of von Hippel-Lindau disease.
